*607737
FIBROBLAST GROWTH FACTOR-BINDING PROTEIN 1; FGFBP1

Alternative titles; symbols
FGF-BINDING PROTEIN 1; FGFBP
HEPARIN-BINDING GROWTH FACTOR-BINDING PROTEIN, 17-KD; HBP17
HBGF-BINDING PROTEIN, 17-KD

HGNC Approved Gene Symbol: FGFBP1

Cytogenetic location: 4p15.32     Genomic coordinates (GRCh37): 4:15,937,191 - 15,939,970 (from NCBI)

TEXT
Description
FGFBP1, or HBP17, binds to both acidic (FGF1; 131220) and basic (FGF2; 134920) fibroblast growth factors in a reversible manner. It also binds to perlecan (HSPG2; 142461).

Cloning
Using affinity chromatography and biochemical analysis, followed by PCR of an epidermoid carcinoma cell line, Wu et al. (1991) isolated a cDNA encoding HBP17. The predicted 234-amino acid secreted protein contains a signal sequence and a potential N-linked glycosylation site. Northern blot analysis revealed expression of a 1.2-kb transcript in epidermoid and squamous carcinoma cells, as well as in normal keratinocytes. Expression was not detected in any other cell lines tested, including nontumorigenic epidermoid cell lines. Immunoblot analysis detected a 17-kD protein that comigrated with FGF2.

Gene Function
By binding analyses, Wu et al. (1991) showed that HBP17 interacts with both FGF1 and FGF2. Like heparin, HBP17 protected both FGF molecules from acid inactivation. HBP17 inhibited the mitogenic activity of FGF1 more efficiently than that of FGF2 in the absence of heparin, and it blocked binding to a liver cell line.

By yeast 2-hybrid and coimmunoprecipitation analyses with domain III of HSPG2 as bait, Mongiat et al. (2001) showed that keratinocyte FGFBP1 interacts with HSPG2. Deletion analysis determined that FGFBP1 binds to the second EGF motif of domain III, close to the binding site for FGF7 (148180). Immunohistochemical analysis demonstrated low-level expression of FGFBP1 in the suprabasal region of the epidermis and higher expression and colocalization with HSPG2 in the pericellular stroma of squamous cell carcinomas.

Mapping
The International Radiation Hybrid Mapping Consortium mapped the FGFBP1 gene to chromosome 4 (D4S3140).

REFERENCES
1. Mongiat, M., Otto, J., Oldershaw, R., Ferrer, F., Sato, J. D., Iozzo, R. V. Fibroblast growth factor-binding protein is a novel partner for perlecan protein core. J. Biol. Chem. 276: 10263-10271, 2001. [PubMed: 11148217, related citations] [Full Text: HighWire Press, Pubget]

2. Wu, D., Kan, M., Sato, G. H., Okamoto, T., Sato, J. D. Characterization and molecular cloning of a putative binding protein for heparin-binding growth factors. J. Biol. Chem. 266: 16778-16785, 1991. [PubMed: 1885605, related citations] [Full Text: HighWire Press, Pubget]

Creation Date: Paul J. Converse : 4/30/2003
Edit History: alopez : 05/09/2005
mgross : 4/30/2003