Entry - *609729 - PDZ DOMAIN-CONTAINING RING FINGER PROTEIN 3; PDZRN3 - OMIM
 
* 609729

PDZ DOMAIN-CONTAINING RING FINGER PROTEIN 3; PDZRN3


Alternative titles; symbols

KIAA1095


HGNC Approved Gene Symbol: PDZRN3

Cytogenetic location: 3p13   Genomic coordinates (GRCh38) : 3:73,382,431-73,624,941 (from NCBI)


TEXT

Cloning and Expression

By sequencing clones obtained from an adult brain cDNA library, Kikuno et al. (1999) cloned PDZRN3, which they designated KIAA1095. The deduced 1,098-amino acid protein contains a C3HC4 zinc finger motif. RT-PCR ELISA detected high expression in heart, whole brain, lung, skeletal muscle, ovary, spinal cord, thalamus, amygdala, and fetal whole brain. Lower expression was detected in kidney, testis, pancreas, adult and fetal liver, and all other specific brain regions tested. Lowest expression was detected in spleen.

By searching for genes encoding proteins structurally similar to LNX (LNX1; 609732) and PDZRN1 (LNX2; 609733), Katoh and Katoh (2004) identified PDZRN3. The deduced 1,066-amino acid protein contains an N-terminal RING domain, followed by 2 PDZ domains and 2 C-terminal bipartite nuclear localization signals. PDZRN3 shares 59.9% amino acid identity with PDZRN4 (609730).


Gene Function

Mesenchymal progenitor cells, such as mouse C2C12 cells, can differentiate into osteoblasts, chondrocytes, adipocytes, or myotubes. Honda et al. (2010) found that osteoblastic differentiation of C2C12 cells induced by human BMP2 (112261) was accompanied by an early increase in Pdzrn3 expression. Furthermore, BMP2-mediated differentiation was enhanced by knockdown of Pdzrn3 via RNA interference. Examination of the signaling pathways involved suggested that Pdzrn3 countered BMP2-mediated differentiation by inhibition of Wnt (see WNT3A; 606359)-beta-catenin (CTNNB1; 116806) signaling. Pdzrn3 suppressed both Lrp6 (603507) expression and Wnt3a-induced phosphorylation of Lrp6, which appeared to be critical for negative regulation of osteoblastic differentiation by Pdzrn3.


Gene Structure

Katoh and Katoh (2004) determined that the PDZRN3 gene contains 10 exons.


Mapping

By genomic sequence analysis, Katoh and Katoh (2004) mapped the PDZRN3 gene to chromosome 3p13.


REFERENCES

  1. Honda, T., Yamamoto, H., Ishii, A., Inui, M. PDZRN3 negatively regulates BMP-2-induced osteoblast differentiation through inhibition of Wnt signaling. Molec. Biol. Cell 21: 3269-3277, 2010. [PubMed: 20668165, images, related citations] [Full Text]

  2. Katoh, M., Katoh, M. Identification and characterization of PDZRN3 and PDZRN4 genes in silico. Int. J. Molec. Med. 13: 607-613, 2004. [PubMed: 15010864, related citations]

  3. Kikuno, R., Nagase, T., Ishikawa, K., Hirosawa, M., Miyajima, N., Tanaka, A., Kotani, H., Nomura, N., Ohara, O. Prediction of the coding sequences of unidentified human genes. XIV. The complete sequences of 100 new cDNA clones from brain which code for large proteins in vitro. DNA Res. 6: 197-205, 1999. [PubMed: 10470851, related citations] [Full Text]


Contributors:
Patricia A. Hartz - updated : 12/6/2011
Creation Date:
Patricia A. Hartz : 11/22/2005
mcolton : 12/18/2013
mgross : 1/13/2012
terry : 12/6/2011
mgross : 11/22/2005
mgross : 11/22/2005

* 609729

PDZ DOMAIN-CONTAINING RING FINGER PROTEIN 3; PDZRN3


Alternative titles; symbols

KIAA1095


HGNC Approved Gene Symbol: PDZRN3

Cytogenetic location: 3p13   Genomic coordinates (GRCh38) : 3:73,382,431-73,624,941 (from NCBI)


TEXT

Cloning and Expression

By sequencing clones obtained from an adult brain cDNA library, Kikuno et al. (1999) cloned PDZRN3, which they designated KIAA1095. The deduced 1,098-amino acid protein contains a C3HC4 zinc finger motif. RT-PCR ELISA detected high expression in heart, whole brain, lung, skeletal muscle, ovary, spinal cord, thalamus, amygdala, and fetal whole brain. Lower expression was detected in kidney, testis, pancreas, adult and fetal liver, and all other specific brain regions tested. Lowest expression was detected in spleen.

By searching for genes encoding proteins structurally similar to LNX (LNX1; 609732) and PDZRN1 (LNX2; 609733), Katoh and Katoh (2004) identified PDZRN3. The deduced 1,066-amino acid protein contains an N-terminal RING domain, followed by 2 PDZ domains and 2 C-terminal bipartite nuclear localization signals. PDZRN3 shares 59.9% amino acid identity with PDZRN4 (609730).


Gene Function

Mesenchymal progenitor cells, such as mouse C2C12 cells, can differentiate into osteoblasts, chondrocytes, adipocytes, or myotubes. Honda et al. (2010) found that osteoblastic differentiation of C2C12 cells induced by human BMP2 (112261) was accompanied by an early increase in Pdzrn3 expression. Furthermore, BMP2-mediated differentiation was enhanced by knockdown of Pdzrn3 via RNA interference. Examination of the signaling pathways involved suggested that Pdzrn3 countered BMP2-mediated differentiation by inhibition of Wnt (see WNT3A; 606359)-beta-catenin (CTNNB1; 116806) signaling. Pdzrn3 suppressed both Lrp6 (603507) expression and Wnt3a-induced phosphorylation of Lrp6, which appeared to be critical for negative regulation of osteoblastic differentiation by Pdzrn3.


Gene Structure

Katoh and Katoh (2004) determined that the PDZRN3 gene contains 10 exons.


Mapping

By genomic sequence analysis, Katoh and Katoh (2004) mapped the PDZRN3 gene to chromosome 3p13.


REFERENCES

  1. Honda, T., Yamamoto, H., Ishii, A., Inui, M. PDZRN3 negatively regulates BMP-2-induced osteoblast differentiation through inhibition of Wnt signaling. Molec. Biol. Cell 21: 3269-3277, 2010. [PubMed: 20668165] [Full Text: https://doi.org/10.1091/mbc.E10-02-0117]

  2. Katoh, M., Katoh, M. Identification and characterization of PDZRN3 and PDZRN4 genes in silico. Int. J. Molec. Med. 13: 607-613, 2004. [PubMed: 15010864]

  3. Kikuno, R., Nagase, T., Ishikawa, K., Hirosawa, M., Miyajima, N., Tanaka, A., Kotani, H., Nomura, N., Ohara, O. Prediction of the coding sequences of unidentified human genes. XIV. The complete sequences of 100 new cDNA clones from brain which code for large proteins in vitro. DNA Res. 6: 197-205, 1999. [PubMed: 10470851] [Full Text: https://doi.org/10.1093/dnares/6.3.197]


Contributors:
Patricia A. Hartz - updated : 12/6/2011

Creation Date:
Patricia A. Hartz : 11/22/2005

Edit History:
mcolton : 12/18/2013
mgross : 1/13/2012
terry : 12/6/2011
mgross : 11/22/2005
mgross : 11/22/2005