Entry - *609892 - RIPPLY TRANSCRIPTIONAL REPRESSOR 3; RIPPLY3 - OMIM
 
* 609892

RIPPLY TRANSCRIPTIONAL REPRESSOR 3; RIPPLY3


Alternative titles; symbols

DOWN SYNDROME CRITICAL REGION GENE 6; DSCR6


HGNC Approved Gene Symbol: RIPPLY3

Cytogenetic location: 21q22.13   Genomic coordinates (GRCh38) : 21:37,006,150-37,019,662 (from NCBI)


TEXT

Cloning and Expression

By database analysis, followed by PCR and 5-prime and 3-prime RACE of fetal tissue cDNA libraries, Shibuya et al. (2000) cloned 4 splice variants of DSCR6, which they designated DSCR6a, DSCR6b, DSCR6c, and DSCR6d. The DSCR6a transcript encodes a deduced 190-amino acid protein; each of the other 3 encode deduced 106-amino acid proteins. PCR analysis detected DSCR6a expression only in fetal kidney. DSCR6b expression was detected in fetal kidney and fetal brain, and at very low levels in a few other tissues.

By searching for sequences similar to that of zebrafish Ripply1 (300575), Kawamura et al. (2005) identified DSCR6, which they called RIPPLY3. The deduced 190-amino acid human protein contains a WRPW tetrapeptide near its N terminus and a conserved domain of about 50 amino acids found in other Ripply proteins.


Mapping

By genomic sequence analysis, Shibuya et al. (2000) mapped the DSCR6 gene to chromosome 21q22.2.


REFERENCES

  1. Kawamura, A., Koshida, S., Hijikata, H., Ohbayashi, A., Kondoh, H., Takada, S. Groucho-associated transcriptional repressor Ripply1 is required for proper transition from the presomitic mesoderm to somites. Dev. Cell 9: 735-744, 2005. [PubMed: 16326386, related citations] [Full Text]

  2. Shibuya, K., Kudoh, J., Minoshima, S., Kawasaki, K., Asakawa, S., Shimizu, N. Isolation of two novel genes, DSCR5 and DSCR6, from Down syndrome critical region on human chromosome 21q22.2. Biochem. Biophys. Res. Commun. 271: 693-698, 2000. [PubMed: 10814524, related citations] [Full Text]


Creation Date:
Patricia A. Hartz : 2/16/2006
mgross : 07/10/2020
alopez : 02/16/2006

* 609892

RIPPLY TRANSCRIPTIONAL REPRESSOR 3; RIPPLY3


Alternative titles; symbols

DOWN SYNDROME CRITICAL REGION GENE 6; DSCR6


HGNC Approved Gene Symbol: RIPPLY3

Cytogenetic location: 21q22.13   Genomic coordinates (GRCh38) : 21:37,006,150-37,019,662 (from NCBI)


TEXT

Cloning and Expression

By database analysis, followed by PCR and 5-prime and 3-prime RACE of fetal tissue cDNA libraries, Shibuya et al. (2000) cloned 4 splice variants of DSCR6, which they designated DSCR6a, DSCR6b, DSCR6c, and DSCR6d. The DSCR6a transcript encodes a deduced 190-amino acid protein; each of the other 3 encode deduced 106-amino acid proteins. PCR analysis detected DSCR6a expression only in fetal kidney. DSCR6b expression was detected in fetal kidney and fetal brain, and at very low levels in a few other tissues.

By searching for sequences similar to that of zebrafish Ripply1 (300575), Kawamura et al. (2005) identified DSCR6, which they called RIPPLY3. The deduced 190-amino acid human protein contains a WRPW tetrapeptide near its N terminus and a conserved domain of about 50 amino acids found in other Ripply proteins.


Mapping

By genomic sequence analysis, Shibuya et al. (2000) mapped the DSCR6 gene to chromosome 21q22.2.


REFERENCES

  1. Kawamura, A., Koshida, S., Hijikata, H., Ohbayashi, A., Kondoh, H., Takada, S. Groucho-associated transcriptional repressor Ripply1 is required for proper transition from the presomitic mesoderm to somites. Dev. Cell 9: 735-744, 2005. [PubMed: 16326386] [Full Text: https://doi.org/10.1016/j.devcel.2005.09.021]

  2. Shibuya, K., Kudoh, J., Minoshima, S., Kawasaki, K., Asakawa, S., Shimizu, N. Isolation of two novel genes, DSCR5 and DSCR6, from Down syndrome critical region on human chromosome 21q22.2. Biochem. Biophys. Res. Commun. 271: 693-698, 2000. [PubMed: 10814524] [Full Text: https://doi.org/10.1006/bbrc.2000.2685]


Creation Date:
Patricia A. Hartz : 2/16/2006

Edit History:
mgross : 07/10/2020
alopez : 02/16/2006